中华中医药杂志(原中国医药学报)2023年2月第38卷第2期CJTCMP,February2023,Vol.38,No.2•679•·临证经验·通信作者:周江,四川省成都市金牛区十二桥路39号成都中医药大学附属医院,邮编:610072,电话:028-81706555E-mail:zhoujiang666@163.com胡天成辨治儿童特发性肺含铁血黄素沉着症思路与方法周江1,胡思樱2,王贵梅3(指导:胡天成1)(1成都中医药大学附属医院,成都610072;2成都中医药大学临床医学院,成都610075;3四川省骨科医院,成都610041)摘要:文章总结了胡天成教授辨病辨证论治儿童特发性肺含铁血黄素沉着症的经验。本病可归属于中医咳喘、血证、虚损等病范畴,病位在肺,与脾肾密切相关;病因多系湿热内蕴;核心病机是湿热熏灼,肺络受损,痰瘀互结;病性以肺脾肾虚为本,湿热痰瘀为标,本虚标实,虚实夹杂。急性肺出血期与慢性反复发作期多实,实证多系湿热痰瘀为患;肺出血静止期、慢性迁延后遗期多虚,虚证多因气血亏虚使然。本病采用辨病辨证相结合,以中药治疗为主的方法,临证应分清标本缓急,总的治疗原则是急则治标,缓则治本;祛邪扶正,补不宜早;以清为主,以通为补。关键词:特发性肺含铁血黄素沉着症;中医;辨证论治;胡天成;名医经验;难治病基金资助:国家重点研发计划(No.2018YFC1704104)HUTian-cheng’sthoughtandmethodofdifferentiationandtreatmentofidiopathicpulmonaryhemosiderosisinchildrenZHOUJiang1,HUSi-ying2,WANGGui-mei3(Advisor:HUTian-cheng1)(1HospitalofChengduUniversityofTCM,Chengdu610072,China;2ClinicalMedicineCollegeofChengduUniversityofTraditionalChineseMedicine,Chengdu610075,China;3SichuanProvinceOrthopedicHospital,Chengdu610041,China)Abstract:ThisarticlesummarizestheexperienceofprofessorHUTian-chengonsyndromedifferentiationinchildrenwithidiopathicpulmonaryhemosiderosis.Thisdiseasecanbeclassifiedintothecategoryofdiseasessuchasexpectoration,bloodsyndrome,anddeficiencyinjuryintraditionalChinesemedicine(TCM),wherethediseaselocationisinthelungandiscloselyrelatedtothespleenandkidney;Etiologymultilineagedampnessheatinternalization;Thecorediseasemechanismisdampnessheatandlavender,lungcollateralsaredamaged,sputumstasisinterposition;Thepathogenicityismarkedbythedeficiencyoflungspleenandkidney,dampness,heatandphlegm...