第一作者简介:邱秋,博士,副主任医师,研究方向:慢性肝病、急性胰腺炎等消化系统疾病研究。E-mail:360894544@qq.com通讯作者:李国均,副主任医师,研究方向:白血病等血液系统恶性疾病。E-mail:289689166@qq.comdoi:10.3969/j.issn.1006-5709.2023.01.024门静脉海绵状瘤胆管病诊治进展邱秋1,刘凯军2,李国均31.重庆市合川区人民医院消化内科,重庆401520;2.陆军军医大学大坪医院消化内科;3.重庆市合川区人民医院血液内科【摘要】门静脉海绵状瘤胆管病(portalcavernomacholangiopathy,PCC)为门静脉海绵状瘤继发的胆管形态结构异常,多见于肝外门静脉阻塞(extrahepaticportalvenousobstruction,EHPVO)患者,其发病机制尚不完全明确,可能与胆道受压、缺血、炎症等有关。磁共振胰胆管造影是其首选检查方法,有症状者可给予内镜治疗、外科手术或介入治疗,但无统一的治疗标准。本文旨在对PCC的发病机制、临床表现、诊断、治疗方式等研究进展作一综述,以期提高临床医师对该病的认识。【关键词】门静脉海绵状瘤胆管病;发病机制;诊断;治疗中图分类号:R575.7文献标识码:A文章编号:1006-5709(2023)01-0114-04收稿日期:2021-08-05AdvanceintreatmentanddiagnosisofportalcavernomacholangiopathyQIUQiu1,LIUKaijun2,LIGuojun31.DepartmentofGastroenterology,People′sHospitalofChongqingHechuan,Chongqing401520;2.DepartmentofGas-troenterology,DapingHospital,ArmyMedicalUniversity;3.DepartmentofHematology,People′sHospitalofChongqingHechuan,China【Abstract】Portalcavernomacholangiopathy(PCC)referstocholangiographicabnormalitiessecondarytoportalcav-ernoma,whichoftenoccursinpatientswithextrahepaticportalvenousobstruction(EHPVD).Itspathogenesisisun-clearandmayberelatedtobileductcompression,ischemiaandinflammation.Magneticresonancecholangiopancreatog-raphyisthefirstchoiceofexamination.Symptomaticpatientscanbegiventoendoscopictreatment,surgeryorinterven-tionaltreatment,however,thereisnoconsistentstandardabouttreatment.Thisreviewaimedtosummarizetheresearchprogressofpathogenesis,clinicalmanifestations,diagnosisandtreatmentmethodsaboutPCCforimprovingtheclini-cians′perception.【Keywords】Portalcavernomacholangiopathy;Pathogenesis;Diagnosis;Treatment门脉高压性胆病(portalbiliopathy,PB)是指门静脉...
